Prueba de porfirina en la orina
La
prueba de uroporfirina mide los niveles de porfirina en la orina. La funcin
ms importante de las porfirinas es como componentes del hem, el
cual est formado por hierro y protoporfirinas. La hemoglobina est
compuesta de cuatro protenas de globina ms cuatro grupos
hem. El oxgeno se adhiere al hierro en las molculas de hem.
Cada paso requiere de la presencia de una enzima. Si cualquiera de las enzimas
es deficiente debido a una enfermedad gentica o a inhibicin
por una sustancia txica, se presenta un tipo de porfiria.
Revision
Last reviewed 2/28/2011 by David C. Dugdale, III, MD, Professor of Medicine, Division of General Medicine, Department of Medicine, University of Washington School of Medicine; and Yi-Bin Chen, MD, Leukemia/Bone Marrow Transplant Program, Massachusetts General Hospital. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc.
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